ENTRY rn00250 Pathway NAME Alanine, aspartate and glutamate metabolism CLASS Metabolism; Amino Acid Metabolism PATHWAY_MAP rn00250 Alanine, aspartate and glutamate metabolism MODULE M00017 Glutamate biosynthesis, oxoglutarate => glutamate (glutamate dehydrogenase) [PATH:rn00250] M00018 Glutamine biosynthesis, glutamate => glutamine [PATH:rn00250] M00019 Glutamate biosynthesis, oxoglutarete => glutamate (glutamate synthase) [PATH:rn00250] M00021 Aspartate biosynthesis, oxaloacetate => aspartate [PATH:rn00250] M00022 Asparagine biosynthesis, aspartate => asparagine [PATH:rn00250] M00026 Alanine biosynthesis, pyruvate => alanine [PATH:rn00250] M00038 Glutamine degradation, glutamine => glutamate + NH3 [PATH:rn00250] M00040 GABA (gamma-Aminobutyrate) shunt [PATH:rn00250] M00044 Aspartate degradation, aspartate => fumarate [PATH:rn00250] M00045 Aspartate degradation, aspartate => oxaloacetate [PATH:rn00250] M00046 Asparagine degradation, asparagine => aspartate +NH3 [PATH:rn00250] DISEASE H00074 Canavan disease (CD) H00185 Citrullinemia (CTLN) H00197 Adenylosuccinate lyase deficiency DBLINKS GO: 0006522 0006531 0006536 REACTION R00093 L-glutamate:NAD+ oxidoreductase (transaminating) R00114 L-Glutamate:NADP+ oxidoreductase (transaminating) R00149 Carbon-dioxide:ammonia ligase (ADP-forming,carbamate-phosphorylating) R00243 L-Glutamate:NAD+ oxidoreductase (deaminating) R00248 L-Glutamate:NADP+ oxidoreductase (deaminating) R00253 L-Glutamate:ammonia ligase (ADP-forming) R00256 L-Glutamine amidohydrolase R00258 L-Alanine:2-oxoglutarate aminotransferase R00261 L-glutamate 1-carboxy-lyase (4-aminobutanoate-forming) R00269 2-Oxoglutaramate amidohydrolase R00348 2-Oxosuccinamate amidohydrolase R00355 L-Aspartate:2-oxoglutarate aminotransferase R00357 L-Aspartic acid:oxygen oxidoreductase (deaminating) R00359 D-Aspartate:oxygen oxidoreductase (deaminating) R00369 L-Alanine:glyoxylate aminotransferase R00396 L-Alanine:NAD+ oxidoreductase (deaminating) R00397 L-aspartate 4-carboxy-lyase (L-alanine-forming) R00400 L-alanine:oxaloacetate aminotransferase R00483 L-aspartate:ammonia ligase (AMP-forming) R00484 N-Carbamoyl-L-aspartate amidohydrolase R00485 L-Asparagine amidohydrolase R00487 Acetyl-CoA:L-aspartate N-acetyltransferase R00488 N-Acetyl-L-aspartate amidohydrolase R00490 L-Aspartate ammonia-lyase R00491 aspartate racemase R00575 hydrogen-carbonate:L-glutamine amido-ligase (ADP-forming, carbamate-phosphorylating) R00576 L-Glutamine:pyruvate aminotransferase R00578 L-aspartate:L-glutamine amido-ligase (AMP-forming) R00707 (S)-1-pyrroline-5-carboxylate:NAD+ oxidoreductase R00708 (S)-1-pyrroline-5-carboxylate:NADP+ oxidoreductase R00713 Succinate-semialdehyde:NAD+ oxidoreductase R00714 Succinate-semialdehyde:NADP+ oxidoreductase R00768 L-glutamine:D-fructose-6-phosphate isomerase (deaminating) R01072 5-phosphoribosylamine:diphosphate phospho-alpha-D-ribosyltransferase (glutamate-amidating) R01083 N6-(1,2-dicarboxyethyl)AMP AMP-lyase (fumarate-forming) R01086 2-(Nomega-L-arginino)succinate arginine-lyase (fumarate-forming) R01135 IMP:L-aspartate ligase (GDP-forming) R01346 L-Asparagine:2-oxo-acid aminotransferase R01397 carbamoyl-phosphate:L-aspartate carbamoyltransferase R01648 4-Aminobutanoate:2-oxoglutarate aminotransferase R01954 L-Citrulline:L-aspartate ligase (AMP-forming) COMPOUND C00014 NH3 C00022 Pyruvate C00025 L-Glutamate C00026 2-Oxoglutarate C00036 Oxaloacetate C00041 L-Alanine C00042 Succinate C00049 L-Aspartate C00064 L-Glutamine C00122 Fumarate C00152 L-Asparagine C00169 Carbamoyl phosphate C00232 Succinate semialdehyde C00334 4-Aminobutanoate C00352 D-Glucosamine 6-phosphate C00402 D-Aspartate C00438 N-Carbamoyl-L-aspartate C00940 2-Oxoglutaramate C01042 N-Acetyl-L-aspartate C02362 2-Oxosuccinamate C03090 5-Phosphoribosylamine C03406 N-(L-Arginino)succinate C03794 N6-(1,2-Dicarboxyethyl)-AMP C03912 (S)-1-Pyrroline-5-carboxylate REFERENCE AUTHORS Nishizuka Y, Seyama Y, Ikai A, Ishimura Y, Kawaguchi A (eds). TITLE [Cellular Functions and Metabolic Maps] (In Japanese) JOURNAL Tokyo Kagaku Dojin (1997) REFERENCE PMID:9687539 AUTHORS Wu G TITLE Intestinal mucosal amino acid catabolism. JOURNAL J Nutr 128:1249-52 (1998) REL_PATHWAY rn00010 Glycolysis / Gluconeogenesis rn00020 Citrate cycle (TCA cycle) rn00230 Purine metabolism rn00240 Pyrimidine metabolism rn00253 Tetracycline biosynthesis rn00260 Glycine, serine and threonine metabolism rn00300 Lysine biosynthesis rn00330 Arginine and proline metabolism rn00340 Histidine metabolism rn00410 beta-Alanine metabolism rn00460 Cyanoamino acid metabolism rn00471 D-Glutamine and D-glutamate metabolism rn00473 D-Alanine metabolism rn00480 Glutathione metabolism rn00650 Butanoate metabolism rn00660 C5-Branched dibasic acid metabolism rn00760 Nicotinate and nicotinamide metabolism rn00770 Pantothenate and CoA biosynthesis rn00860 Porphyrin and chlorophyll metabolism rn00910 Nitrogen metabolism KO_PATHWAY ko00250 ///